methylmalonylkyseliny
Methylmalonyl coenzyme A (CoA), also known as methylmalonyl-KS, is a crucial intermediate in the metabolism of fatty acids and amino acids. It is involved in the breakdown of these molecules to generate energy for the cell. The methylmalonyl-CoA molecule is formed when the beta-oxidation of fatty acids results in the production of succinyl-CoA, which is then methylated to form methylmalonyl-CoA.
This process is catalyzed by the enzyme methylmalonyl-CoA mutase, a vitamin B12-dependent enzyme. The methylmalonyl-CoA molecule
Methylmalonyl-CoA has been linked to various diseases and conditions, including propionic acidemia, a rare genetic disorder
From a nutritional perspective, methylmalonyl-CoA is of interest due to its role in the metabolism of dietary
In conclusion, methylmalonyl-CoA is a key intermediate in the breakdown of fatty acids and amino acids, playing