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ovotesticular

Ovotesticular refers to a condition in which an individual has both ovarian and testicular tissue, either within the same gonad (ovotestis) or in two gonads (one ovary and one testis). In medical usage, this is described as an ovotesticular disorder of sex development (DSD). It is a rare condition, most often associated with mosaic karyotypes such as 46,XX/46,XY, although other chromosomal patterns can occur.

Clinical presentation is variable. Some people have predominantly female-appearing external genitalia with internal gonads that include

Diagnosis involves a combination of history and examination, karyotype analysis, endocrine testing, imaging to locate gonads,

Management requires a multidisciplinary team. Approaches are individualized and may include decisions about sex of rearing,

Prognosis is variable and depends on anatomy, tissue function, and psychosocial support. With contemporary multidisciplinary care,

ovotestes;
others
have
ambiguous
genitalia
or
a
mix
of
male-
and
female-typical
features.
Puberty
and
reproductive
potential
depend
on
the
function
of
the
gonadal
tissue
and
the
presence
of
a
functioning
uterus
and
fallopian
tubes,
when
applicable.
and
histopathology
when
gonadal
tissue
is
removed
or
biopsied.
The
aim
is
to
determine
the
anatomy
and
underlying
genetics
to
guide
management.
hormone
therapy
for
puberty,
and
surgical
considerations
to
align
genital
appearance
with
gender
identity
or
to
preserve
reproductive
potential.
Some
dysgenetic
tissue
carries
an
elevated
risk
of
germ
cell
tumors,
so
clinicians
may
recommend
surveillance
or
removal
of
such
tissue
in
certain
cases.
many
individuals
with
ovotesticular
DSD
adapt
well
and
achieve
a
sense
of
well-being
and
identity
that
aligns
with
their
lived
experience.